oasthouse urine disease

An inherited metabolic defect in the absorption of methionine which is converted by intestinal bacteria to alpha-hydroxybutyric acid; characterised by diarrhoea, tachypnea, and marked urinary excretion of alpha-hydroxybutyric acid (causing an odour like that of an oasthouse). ... Origin: oast, kiln for drying hops, malt, or tobacco ... (05 Mar 2000...
Found on http://www.encyclo.co.uk/local/20973

oasthouse urine disease

(ōst´hows) methionine malabsorption syndrome.
Found on http://www.encyclo.co.uk/local/21001

oasthouse urine disease

Type: Term Definitions: 1. an autosomal recessively inherited metabolic defect in the absorption of methionine that is converted by intestinal bacteria to α-hydroxybutyric acid; characterized by diarrhea, tachypnea, and marked urinary excretion of α-hydroxybutyric acid (causing an odor like that of an oasthouse).
Found on http://www.medilexicon.com/medicaldictionary.php?t=25695
No exact match found